TRANSTHYRETIN CARDIAC AMYLOIDOSIS REVEALED BY MULTIMODALITY IMAGING IN AN ELDERLY PATIENT WITH HFpEF

Le Quoc Hung 1 , , Tran Trong Phu 2 , Nguyen Van Be Hai 1 , Tran Huong Tra My 1 , Nguyen Van Te 3
1 Bệnh viện Thống Nhất image/svg+xml
2 Trường Đại học Khoa học Tự nhiên, Đại học Quốc gia Thành phố Hồ Chí Minh image/svg+xml
3 Franco-Vietnamese Hospital, Ho Chi Minh City
* Tác giả liên hệ:

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Lượt tải: 10 Lượt xem: 46
DOI
10.63947/bvtn.v2i7.17
Xuất bản
27-02-2026
Số Tập 2 Số 7 (2026): Multimodal approaches in geriatrics
Chuyên mục
Báo cáo ca lâm sàng
Danh mục
Nghiên cứu khoa học

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1.
Quoc Hung L, Trong Phu T, Van Be Hai N, Huong Tra My T, Van Te N. TRANSTHYRETIN CARDIAC AMYLOIDOSIS REVEALED BY MULTIMODALITY IMAGING IN AN ELDERLY PATIENT WITH HFpEF. JHA [Internet]. Vietnam; 2026 tháng 2 27 [cited 2026 tháng 2 28];2(7):131–136. https://tcsuckhoelaohoa.vn/bvtn/article/view/184 doi: 10.63947/bvtn.v2i7.17
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Tóm tắt

Amyloid cardiomyopathy is an infiltrative disease caused by extracellular deposition of amyloid fibrils within the myocardium, most commonly from immunoglobulin light-chain (AL) or transthyretin (ATTR) sources, leading to progressive heart failure, arrhythmias, and conduction disturbances. We present the case of an 80-year-old man with heart failure with preserved ejection fraction (HFpEF) and comorbidities who was admitted for acute onset dyspnea accompanied by profound hypotension at home. Together with a non-clonal free light-chain profile, these findings supported a diagnosis of transthyretin (ATTR) cardiac amyloidosis. This case highlights the value of integrating electrocardiogram, echocardiography, cardiac magnetic resonance, and bone-avid tracer scintigraphy to establish the diagnosis of ATTR cardiomyopathy and guide management in settings where disease-modifying therapy remains limited.Keywords: supraclavicular brachial plexus nerve block, adductor canal block, popliteal sciatic block, heart failure, limb amputation.

Từ khóa

Amyloid cardiomyopathy transthyretin scintigraphy

Tài liệu tham khảo

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